Background: Duchenne muscular dystrophy (DMD) is a progressive muscle disease. No curative therapy is currently available, but in recent decades standards of care have improved. These improvements include the use of corticosteroids and mechanical ventilation. Objective: To present a detailed population based report of the DMD disease course in The Netherlands (1980–2006) and evaluate the effect of changes in care by comparing it with an historical Dutch DMD cohort (1961–1974). Methods: Information about DMD patients was gathered through the Dutch Dystrophinopathy Database using a standardized... Mehr ...
| Verfasser: |
van den Bergen, J. C.
Ginjaar, H. B.
Van Essen, A. J.
Pangalila, R.
De Groot, I. J.M.
Wijkstra, P. J.
Zijnen, M. P.
Cobben, N. A.M.
Kampelmacher, M. J.
Wokke, B. H.A.
de Coo, I. F.M.
Fock, J. M.
Horemans, A. M.C.
van Tol, M.
Vroom, E.
Rijlaarsdam, M. E.B.
Straathof, C. S.M.
Niks, E. H.
Verschuuren, J. J.G.M. |
| Dokumenttyp: |
Artikel |
| Erscheinungsdatum: |
2014 |
| Reihe/Periodikum: |
van den Bergen , J C , Ginjaar , H B , Van Essen , A J , Pangalila , R , De Groot , I J M , Wijkstra , P J , Zijnen , M P , Cobben , N A M , Kampelmacher , M J , Wokke , B H A , de Coo , I F M , Fock , J M , Horemans , A M C , van Tol , M , Vroom , E , Rijlaarsdam , M E B , Straathof , C S M , Niks , E H & Verschuuren , J J G M 2014 , ' Forty-five years of Duchenne muscular dystrophy in The Netherlands ' , Journal of Neuromuscular Diseases , vol. 1 , no. 1 , pp. 99-109 . https://doi.org/10.3233/JND-140005 |
| Schlagwörter: |
Corticosteroids
/ Duchenne muscular dystrophy
/ Mechanical home ventilation
/ Natural history
/ Survival |
| Sprache: |
Englisch |
| Permalink: |
https://search.fid-benelux.de/Record/base-29192307 |
| Datenquelle: |
BASE;
Originalkatalog |
| Powered By: |
BASE |
| Link(s) :
|
https://hdl.handle.net/11370/c217de5d-ae4e-480d-8672-e40a58ac5751 |
