Real-life experience of familial fibrosis in a Belgian university

Introduction Familial pulmonary fibrosis (FPF) is defined as lung fibrosis affecting at least 2 members of the 1st degree of a family. Monogenic pulmonary fibrosis is usually investigated in this case and/or when an idiopathic interstitial lung disease occurs in a patient younger than 55 years-old, eventually associated with extra-thoracic involvement. We reviewed all FPF cases seen in our university (2 tertiary hospitals) in 2017 and 2018. Methods All FPF patients and an equal number of sporadic idiopathic pulmonary fibrosis (IPF) diagnosed between January 1st 2017 and December 31st 2018 were... Mehr ...